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Dopa-responsive dystonia: a syndrome of selective nigrostriatal dopaminergic deficiency.
Dopa-responsive dystonia (DRD) is no longer a rare oddity. For the clinician, DRD poses a diagnostic challenge as its clinical presentation can be quite diverse. Marked and sustained response to L-dopa is the most crucial and absolute hallmark in confirming a diagnosis. Absence of degenerative nigra...
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Autor principal: | |
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Formato: | Artigo |
Idioma: | Inglês |
Publicado em: |
Korean Academy of Medical Sciences
1997
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Assuntos: | |
Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3054207/ https://ncbi.nlm.nih.gov/pubmed/9288624 |
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