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Dopa-responsive dystonia: a syndrome of selective nigrostriatal dopaminergic deficiency.

Dopa-responsive dystonia (DRD) is no longer a rare oddity. For the clinician, DRD poses a diagnostic challenge as its clinical presentation can be quite diverse. Marked and sustained response to L-dopa is the most crucial and absolute hallmark in confirming a diagnosis. Absence of degenerative nigra...

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Detalhes bibliográficos
Autor principal: Jeon, B. S.
Formato: Artigo
Idioma:Inglês
Publicado em: Korean Academy of Medical Sciences 1997
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3054207/
https://ncbi.nlm.nih.gov/pubmed/9288624
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