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Characterization of Atp1a3 mutant mice as a model of rapid-onset dystonia with parkinsonism

Rapid-onset dystonia with parkinsonism (RDP) or DYT12 dystonia is a rare form of primary, generalized dystonia. Patients do not present with any symptoms until triggered by a physiological stressor. Within days, patients will show both dystonia and Parkinson’s disease. Missense mutations resulting i...

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Detalhes bibliográficos
Main Authors: DeAndrade, Mark P., Yokoi, Fumiaki, van Groen, Thomas, Lingrel, Jerry B., Li, Yuqing
Formato: Artigo
Idioma:Inglês
Publicado em: 2010
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2981691/
https://ncbi.nlm.nih.gov/pubmed/20850480
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbr.2010.09.009
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