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X-linked lymphoproliferative syndromes: brothers or distant cousins?

X-linked lymphoproliferative disease (XLP1), described in the mid-1970s and molecularly defined in 1998, and XLP2, reported in 2006, are prematurely lethal genetic immunodeficiencies that share susceptibility to overwhelming inflammatory responses to certain infectious triggers. Signaling lymphocyti...

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Bibliografske podrobnosti
Main Authors: Filipovich, Alexandra H., Zhang, Kejian, Snow, Andrew L., Marsh, Rebecca A.
Format: Artigo
Jezik:Inglês
Izdano: American Society of Hematology 2010
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC2981470/
https://ncbi.nlm.nih.gov/pubmed/20660790
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2010-03-275909
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