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Impaired hepatic drug and steroid metabolism in congenital adrenal hyperplasia due to P450 oxidoreductase deficiency

OBJECTIVE: Patients with congenital adrenal hyperplasia due to P450 oxidoreductase (POR) deficiency (ORD) present with disordered sex development and glucocorticoid deficiency. This is due to disruption of electron transfer from mutant POR to microsomal cytochrome P450 (CYP) enzymes that play a key...

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Библиографические подробности
Главные авторы: Tomalik-Scharte, Dorota, Maiter, Dominique, Kirchheiner, Julia, Ivison, Hannah E, Fuhr, Uwe, Arlt, Wiebke
Формат: Artigo
Язык:Inglês
Опубликовано: BioScientifica 2010
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC2977993/
https://ncbi.nlm.nih.gov/pubmed/20844025
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1530/EJE-10-0764
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