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Altered sulfhydryl reactivity of hemoglobins and red blood cell membranes in congenital heinz body hemolytic anemia

The mechanisms of hemoglobin precipitation into Heinz bodies and hemolytic anemia that characterize congenital Heinz body hemolytic anemia (CHBHA) were studied in patients with the unstable hemoglobins, Köln (β-98 valine → methionine) and Hammersmith (β-42 phenylalanine → serine). The cysteines in t...

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Publicado en:J Clin Invest
Autores principales: Jacob, Harry S., Brain, Michael C., Dacie, John V.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society for Clinical Investigation 1968
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Acceso en línea:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC297438/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/5725279/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI105950
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