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Plasma levels of C1- inhibitor complexes and cleaved C1- inhibitor in patients with hereditary angioneurotic edema.

C1- inhibitor (C1(-)-Inh) catabolism in plasma of patients with hereditary angioneurotic edema (HANE) was assessed by measuring the complexes formed by C1(-)-Inh with its target proteases (C1-s, Factor XIIa, and kallikrein) and a modified (cleaved) inactive form of C1(-)-Inh (iC1(-)-Inh). This study...

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Detalhes bibliográficos
Publicado no:J Clin Invest
Principais autores: Cugno, M, Nuijens, J, Hack, E, Eerenberg, A, Frangi, D, Agostoni, A, Cicardi, M
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Clinical Investigation 1990
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC296554/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2318974/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI114555
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