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The Alpha Granule Proteome: Novel Proteins in Normal and Ghost Granules in Gray Platelet Syndrome

BACKGROUND: Deficiencies in granule-bound substances in platelets cause congenital bleeding disorders known as storage pool deficiencies. For disorders such as Gray Platelet syndrome (GPS), in which thrombocytopenia, enlarged platelets, and a paucity of alpha granules are observed, only the clinical...

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Autores principales: Maynard, Dawn M., Heijnen, Harry F. G., Gahl, William A., Gunay-Aygun, Meral
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2953603/
https://ncbi.nlm.nih.gov/pubmed/20524979
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1538-7836.2010.03932.x
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