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INTERACTION AND LOCALIZATION OF THE RETINITIS PIGMENTOSA PROTEIN RP2 AND NSF IN RETINAL PHOTORECEPTOR CELLS

RP2 is a ubiquitously expressed protein encoded by a gene associated with X-linked retinitis pigmentosa (XLRP), a retinal degenerative disease that causes severe vision loss. Previous in vitro studies have shown that RP2 binds to ADP ribosylation factor-like 3 (Arl3) and activates its intrinsic GTPa...

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Autores principales: Holopainen, Juha M., Cheng, Christiana L., Molday, Laurie L., Johal, Gurp, Coleman, Jonathan, Dyka, Frank, Hii, Theresa, Ahn, Jinhi, Molday, Robert S.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2942077/
https://ncbi.nlm.nih.gov/pubmed/20669900
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/bi1005249
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