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Adiposity is increased among High-Functioning, Non-Ambulatory Patients with Spinal Muscular Atrophy

The relationship between body composition and function in spinal muscular atrophy (SMA) is poorly understood. 53 subjects with SMA were stratified by type and Hammersmith Functional Motor Scale, Expanded score into three cohorts: Low-Functioning Non-Ambulatory (type 2 with Hammersmith score <12,...

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Autori principali: Sproule, Douglas M., Montes, Jacqueline, Dunaway, Sally, Montgomery, Megan, Battista, Vanessa, Koenigsberger, Dorcas, Martens, Bill, Shen, Wei, Punyanitya, Mark, Benton, Maryjane, Butler, Hailly, Caracciolo, Jayson, Mercuri, Eugenio, Finkel, Richard, Darras, Basil, De Vivo, Darryl C., Kaufmann, Petra
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2902766/
https://ncbi.nlm.nih.gov/pubmed/20610154
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nmd.2010.05.013
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