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Microfibril Structure Masks Fibrillin-2 in Postnatal Tissues

Fibrillin microfibrils are polymeric structures present in connective tissues. The importance of fibrillin microfibrils to connective tissue function has been demonstrated by the multiple genetic disorders caused by mutations in fibrillins and in microfibril-associated molecules. However, knowledge...

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Main Authors: Charbonneau, Noe L., Jordan, C. Diana, Keene, Douglas R., Lee-Arteaga, Sui, Dietz, Harry C., Rifkin, Daniel B., Ramirez, Francesco, Sakai, Lynn Y.
Formato: Artigo
Idioma:Inglês
Publicado: American Society for Biochemistry and Molecular Biology 2010
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC2888437/
https://ncbi.nlm.nih.gov/pubmed/20404337
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M109.087031
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