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Microfibril Structure Masks Fibrillin-2 in Postnatal Tissues

Fibrillin microfibrils are polymeric structures present in connective tissues. The importance of fibrillin microfibrils to connective tissue function has been demonstrated by the multiple genetic disorders caused by mutations in fibrillins and in microfibril-associated molecules. However, knowledge...

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Bibliografski detalji
Glavni autori: Charbonneau, Noe L., Jordan, C. Diana, Keene, Douglas R., Lee-Arteaga, Sui, Dietz, Harry C., Rifkin, Daniel B., Ramirez, Francesco, Sakai, Lynn Y.
Format: Artigo
Jezik:Inglês
Izdano: American Society for Biochemistry and Molecular Biology 2010
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2888437/
https://ncbi.nlm.nih.gov/pubmed/20404337
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M109.087031
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