Gray platelet syndrome. Dissociation between abnormal sorting in megakaryocyte alpha-granules and normal sorting in Weibel-Palade bodies of endothelial cells.

The gray platelet syndrome (GPS) is a rare congenital bleeding disorder in which megakaryocytes and platelets are deficient in alpha-granule secretory proteins. Since the Weibel-Palade bodies (WPB) of endothelial cells as well as the alpha-granules contain the von Willebrand Factor (vWF) and P-selec...

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Pubblicato in:	J Clin Invest
Autori principali:	Gebrane-Younès, J, Cramer, E M, Orcel, L, Caen, J P
Natura:	Artigo
Lingua:	Inglês
Pubblicazione:	American Society for Clinical Investigation 1993
Soggetti:	Research Article
Accesso online:	https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC288507/ https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/7504696/ https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI116926
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