Caricamento...

Biallelic TSC gene inactivation in tuberous sclerosis complex

BACKGROUND: A pivotal developmental question is whether tubers in tuberous sclerosis complex (TSC) form by germline and somatic TSC1 or TSC2 gene mutations. Loss of TSC1 or TSC2 in vitro and in vivo leads to mTORC1 cascade activation and ribosomal protein S6 phosphorylation (P-S6). Giant cells (GCs)...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Crino, Peter B., Aronica, Eleonora, Baltuch, Gordon, Nathanson, Katherine L.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Academy of Neurology 2010
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2882213/
https://ncbi.nlm.nih.gov/pubmed/20498439
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1212/WNL.0b013e3181e04325
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !