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Pathogenesis of permeability barrier abnormalities in the ichthyoses: inherited disorders of lipid metabolism

Many of the ichthyoses are associated with inherited disorders of lipid metabolism. These disorders have provided unique models to dissect physiologic processes in normal epidermis and the pathophysiology of more common scaling conditions. In most of these disorders, a permeability barrier abnormali...

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Autores principales: Elias, Peter M., Williams, Mary L., Holleran, Walter M., Jiang, Yan J., Schmuth, Matthias
Formato: Artigo
Lenguaje:Inglês
Publicado: 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2844331/
https://ncbi.nlm.nih.gov/pubmed/18245815
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.R800002-JLR200
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