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Pathogenesis of permeability barrier abnormalities in the ichthyoses: inherited disorders of lipid metabolism

Many of the ichthyoses are associated with inherited disorders of lipid metabolism. These disorders have provided unique models to dissect physiologic processes in normal epidermis and the pathophysiology of more common scaling conditions. In most of these disorders, a permeability barrier abnormali...

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Sonraí Bibleagrafaíochta
Main Authors: Elias, Peter M., Williams, Mary L., Holleran, Walter M., Jiang, Yan J., Schmuth, Matthias
Formáid: Artigo
Teanga:Inglês
Foilsithe: 2008
Ábhair:
Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC2844331/
https://ncbi.nlm.nih.gov/pubmed/18245815
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.R800002-JLR200
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