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Optimal dietary therapy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency

Current dietary therapy for long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) or trifunctional protein (TFP) deficiency consists of fasting avoidance, and limiting long-chain fatty acid (LCFA) intake. This study reports the relationship of dietary intake and metabolic control as measured by plasma...

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Detalhes bibliográficos
Main Authors: Gillingham, Melanie B., Connor, William E., Matern, Dietrich, Rinaldo, Piero, Burlingame, Terry, Meeuws, Kaatje, Harding, Cary O.
Formato: Artigo
Idioma:Inglês
Publicado em: 2003
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2813192/
https://ncbi.nlm.nih.gov/pubmed/12809642
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