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Peutz-Jeghers syndrome: Diagnostic and therapeutic approach

Peutz-Jeghers syndrome (PJS) is an inherited, autosomal dominant disorder distinguished by hamartomatous polyps in the gastrointestinal tract and pigmented mucocutaneous lesions. Prevalence of PJS is estimated from 1 in 8300 to 1 in 280 000 individuals. PJS predisposes sufferers to various malignanc...

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Autors principals: Kopacova, Marcela, Tacheci, Ilja, Rejchrt, Stanislav, Bures, Jan
Format: Artigo
Idioma:Inglês
Publicat: The WJG Press and Baishideng 2009
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2778095/
https://ncbi.nlm.nih.gov/pubmed/19916169
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3748/wjg.15.5397
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