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Severe Osteogenesis Imperfecta in Cyclophilin B–Deficient Mice

Osteogenesis Imperfecta (OI) is a human syndrome characterized by exquisitely fragile bones due to osteoporosis. The majority of autosomal dominant OI cases result from point or splice site mutations in the type I collagen genes, which are thought to lead to aberrant osteoid within developing bones....

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Detalhes bibliográficos
Main Authors: Choi, Jae Won, Sutor, Shari L., Lindquist, Lonn, Evans, Glenda L., Madden, Benjamin J., Bergen, H. Robert, Hefferan, Theresa E., Yaszemski, Michael J., Bram, Richard J.
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2009
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2777385/
https://ncbi.nlm.nih.gov/pubmed/19997487
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pgen.1000750
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