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CEP290 interacts with the centriolar satellite component PCM-1 and is required for Rab8 localization to the primary cilium

Joubert syndrome (JS) is a developmental brain disorder characterized by cerebellar vermis hypoplasia, abnormal eye movement, ataxia and mental retardation. Mutations in CEP290 mutations are responsible for the cerebello–oculo–renal subtype of JS that includes kidney cysts and retinal degeneration,...

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Библиографические подробности
Главные авторы: Kim, Joon, Krishnaswami, Suguna Rani, Gleeson, Joseph G.
Формат: Artigo
Язык:Inglês
Опубликовано: Oxford University Press 2008
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC2722899/
https://ncbi.nlm.nih.gov/pubmed/18772192
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddn277
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