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Genetic Defects of Apoptosis and Primary Immunodeficiency
Programmed cell death is important for maintaining lymphocyte homeostasis. Several human inherited diseases with impaired apoptosis have been identified at the genetic level: autoimmune lymphoproliferative syndrome (ALPS), caspase-8 deficiency state (CEDS), and X-linked lymphoproliferative syndrome...
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| Asıl Yazarlar: | , |
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| Materyal Türü: | Artigo |
| Dil: | Inglês |
| Baskı/Yayın Bilgisi: |
2008
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| Konular: | |
| Online Erişim: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2671802/ https://ncbi.nlm.nih.gov/pubmed/18424336 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.iac.2008.01.002 |
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