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Impaired recovery of dysferlin-null skeletal muscle after contraction-induced injury in vivo

The protein, dysferlin, mediates sarcolemmal repair in vitro, implicating defective membrane repair in dysferlinopathies. To study the role of dysferlin in vivo, we assessed contractile function, sarcolemmal integrity, and myogenesis before and after injury from large-strain lengthening contractions...

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Hlavní autoři: Roche, Joseph A., Lovering, Richard M., Bloch, Robert J.
Médium: Artigo
Jazyk:Inglês
Vydáno: 2008
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2662728/
https://ncbi.nlm.nih.gov/pubmed/18815587
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/WNR.0b013e328311ca35
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