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Nevoid basal cell carcinoma syndrome (Gorlin syndrome)

Nevoid basal cell carcinoma syndrome (NBCCS), also known as Gorlin syndrome, is a hereditary condition characterized by a wide range of developmental abnormalities and a predisposition to neoplasms. The estimated prevalence varies from 1/57,000 to 1/256,000, with a male-to-female ratio of 1:1. Main...

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Autor principal: Lo Muzio, Lorenzo
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2008
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2607262/
https://ncbi.nlm.nih.gov/pubmed/19032739
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1750-1172-3-32
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