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Anaesthesiologic protocol for kidney transplantation in two patients with Fabry Disease: a case series

Fabry's Disease is a rare genetic syndrome, with a classic X-linked alpha -galactosidase A deficiency phenotype, responsible for glico-sphyngolypids metabolism impairment with clinical effects in several organs and functions. We describe the anaesthesiologic implications of two patients with Fa...

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Bibliografske podrobnosti
Main Authors: Sorbello, Massimiliano, Veroux, Massimiliano, Cutuli, Melania, Morello, Gianluigi, Paratore, Annalaura, Sidoti, Mirko Tindaro, Maugeri, Jessica Giuseppina, Gagliano, Massimiliano, Giuffrida, Giuseppe, Corona, Daniela, Veroux, Pierfrancesco
Format: Artigo
Jezik:Inglês
Izdano: BioMed Central 2008
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC2596113/
https://ncbi.nlm.nih.gov/pubmed/19014714
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1757-1626-1-321
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