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Multiple roles for emerin: implications for Emery-Dreifuss muscular dystrophy

X-linked Emery-Dreifuss muscular dystrophy (X-EDMD) is inherited through mutations in EMD, which encodes a nuclear membrane protein named emerin. Emerin is expressed in most cells, but EDMD strikes specific tissues. This review summarizes growing evidence that emerin has roles in both tissue-specifi...

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Detalhes bibliográficos
Main Authors: Holaska, James M., Wilson, Katherine L.
Formato: Artigo
Idioma:Inglês
Publicado em: 2006
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2559942/
https://ncbi.nlm.nih.gov/pubmed/16761279
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ar.a.20334
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