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Role of Stargardt-3 macular dystrophy protein (ELOVL4) in the biosynthesis of very long chain fatty acids

Stargardt-like macular dystrophy (STGD3) is a dominantly inherited juvenile macular degeneration that eventually leads to loss of vision. Three independent mutations causing STGD3 have been identified in exon six of a gene named Elongation of very long chain fatty acids 4 (ELOVL4). The ELOVL4 protei...

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Autores principales: Agbaga, Martin-Paul, Brush, Richard S., Mandal, Md Nawajes A., Henry, Kimberly, Elliott, Michael H., Anderson, Robert E.
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2525561/
https://ncbi.nlm.nih.gov/pubmed/18728184
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0802607105
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