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Mitochondrial Ca(2+) homeostasis in lysosomal storage diseases
Lysosomal storage diseases (LSDs) are a class of genetic disorders in which proteins responsible for digestion or absorption of endocytosed material do not function or do not localize properly. The resulting cellular “indigestion” causes buildup of intracellular storage inclusions that contain unpro...
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| Autores principales: | , |
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| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
2008
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2517575/ https://ncbi.nlm.nih.gov/pubmed/18242695 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ceca.2007.12.005 |
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