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Mitochondrial Ca(2+) homeostasis in lysosomal storage diseases

Lysosomal storage diseases (LSDs) are a class of genetic disorders in which proteins responsible for digestion or absorption of endocytosed material do not function or do not localize properly. The resulting cellular “indigestion” causes buildup of intracellular storage inclusions that contain unpro...

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Autores principales: Kiselyov, Kirill, Muallem, Shmuel
Formato: Artigo
Lenguaje:Inglês
Publicado: 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2517575/
https://ncbi.nlm.nih.gov/pubmed/18242695
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ceca.2007.12.005
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