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Allele and species dependent contractile defects by restrictive and hypertrophic cardiomyopathy-linked troponin I mutants

Restrictive cardiomyopathy (RCM) is a debilitating disease characterized by impaired ventricular filling, reduced ventricular volumes, and severe diastolic dysfunction. Hypertrophic cardiomyopathy (HCM) is characterized by ventricular hypertrophy and heightened risk of premature sudden cardiac death...

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Detalhes bibliográficos
Main Authors: Davis, Jennifer, Wen, Haitao, Edwards, Terri, Metzger, Joseph M.
Formato: Artigo
Idioma:Inglês
Publicado em: 2008
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2443058/
https://ncbi.nlm.nih.gov/pubmed/18423659
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.yjmcc.2008.02.274
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