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Hereditary deficiency of the seventh component of complement and recurrent meningococcal infection: investigations of an Irish family using a novel haemolytic screening assay for complement activity and C7 M/N allotyping.

Terminal complement component deficiency predisposes to meningococcal infection and is inherited in an autosomal co-dominant manner. An Irish family is described, in which 2 of 3 brothers had recurrent meningococcal infection. A novel screening assay was used to investigate for terminal complement d...

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Autores principales: Egan, L. J., Orren, A., Doherty, J., Würzner, R., McCarthy, C. F.
Formato: Artigo
Lenguaje:Inglês
Publicado: Cambridge University Press 1994
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2271528/
https://ncbi.nlm.nih.gov/pubmed/7523157
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