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HURLER'S SYNDROME : EFFECT OF RETINOL (VITAMIN A ALCOHOL) ON CELLULAR MUCOPOLYSACCHARIDES IN CULTURED HUMAN SKIN FIBROBLASTS

Skin fibroblasts from eight families with Hurler's syndrome (X-linked recessive and autosomal recessive) and normal individuals have been studied in cell culture. A good correlation between cellular metachromasia and the quantitative estimation of intracellular mucopolysaccharides was observed...

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Detaylı Bibliyografya
Asıl Yazarlar: Danes, B. Shannon, Bearn, Alexander G.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: The Rockefeller University Press 1966
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC2138335/
https://ncbi.nlm.nih.gov/pubmed/4224371
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