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Spontaneous Murine Neuroaxonal Dystrophy: a Model of Infantile Neuroaxonal Dystrophy

The neuroaxonal dystrophies (NADs) in human beings are fatal, inherited, neurodegenerative diseases with distinctive pathological features. This report describes a new mouse model of NAD that was identified as a spontaneous mutation in a BALB/c congenic mouse strain. The affected animals developed c...

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Dettagli Bibliografici
Autori principali: Bouley, D. M., McIntire, J. J., Harris, B. T., Tolwani, R. J., Otto, G. M., DeKruyff, R. H., Hayflick, S. J.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2006
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2099456/
https://ncbi.nlm.nih.gov/pubmed/16542671
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jcpa.2005.10.002
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