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Recurrent pneumonia with mild hypogammaglobulinemia diagnosed as X-linked agammaglobulinemia in adults

BACKGROUND: X-linked agammaglobulinemia (XLA) is a humoral immunodeficiency caused by disruption of the Bruton's tyrosine kinase (BTK) gene. Typical XLA patients suffer recurrent and severe bacterial infections in childhood. METHODS: Flow cytometric analysis of the peripheral monocytes using th...

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Autors principals: Usui, Kazuhiro, Sasahara, Yoji, Tazawa, Ryushi, Hagiwara, Koichi, Tsukada, Satoshi, Miyawaki, Toshio, Tsuchiya, Shigeru, Nukiwa, Toshihiro
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2001
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2092384/
https://ncbi.nlm.nih.gov/pubmed/11686883
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/rr56
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