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Torn apart: membrane rupture in muscular dystrophies and associated cardiomyopathies

Muscular dystrophies are often caused by mutations in cytoskeletal proteins that render cells more susceptible to strain-induced injury in mechanically active tissues such as skeletal or cardiac muscle. In this issue of the JCI, Han et al. report that dysferlin participates in membrane resealing in...

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Detalles Bibliográficos
Autores principales: Lammerding, Jan, Lee, Richard T.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society for Clinical Investigation 2007
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC1904332/
https://ncbi.nlm.nih.gov/pubmed/17607350
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI32686
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