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Polycystic Kidney Rat Is a Novel Animal Model of Caroli’s Disease Associated with Congenital Hepatic Fibrosis

Caroli’s disease (congenital intrahepatic biliary dilatation) associated with congenital hepatic fibrosis is an autosomal recessive polycystic kidney disease. Recently, the polycystic kidney (PCK) rat, a spontaneous mutant derived from a colony of Crj:CD rats with polycystic lesions in the liver and...

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Autori principali: Sanzen, Takahiro, Harada, Kenichi, Yasoshima, Mitsue, Kawamura, Yasuhito, Ishibashi, Masahiko, Nakanuma, Yasuni
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Investigative Pathology 2001
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1891952/
https://ncbi.nlm.nih.gov/pubmed/11337358
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