Impaired Elastogenesis in Hurler Disease : Dermatan Sulfate Accumulation Linked to Deficiency in Elastin-Binding Protein and Elastic Fiber Assembly

Ítems similars

• Retrovirally Mediated Overexpression of Versican V3 Reverses Impaired Elastogenesis and Heightened Proliferation Exhibited by Fibroblasts from Costello Syndrome and Hurler Disease Patients
  per: Hinek, Aleksander, et al.
  Publicat: (2004)
• Impaired Elastic-Fiber Assembly by Fibroblasts from Patients with Either Morquio B Disease or Infantile GM1-Gangliosidosis Is Linked to Deficiency in the 67-kD Spliced Variant of β-Galactosidase
  per: Hinek, Aleksander, et al.
  Publicat: (2000)
• Impaired elastin fiber assembly related to reduced 67-kD elastin-binding protein in fetal lamb ductus arteriosus and in cultured aortic smooth muscle cells treated with chondroitin sulfate.
  per: Hinek, A, et al.
  Publicat: (1991)
• Neuraminidase-1 is required for the normal assembly of elastic fibers
  per: Starcher, Barry, et al.
  Publicat: (2008)
• Transglutaminase-Mediated Cross-Linking of Tropoelastin to Fibrillin Stabilises the Elastin Precursor Prior to Elastic Fibre Assembly
  per: Lockhart-Cairns, Michael P., et al.
  Publicat: (2020)