The crystal structure of palmitoyl protein thioesterase 1 and the molecular basis of infantile neuronal ceroid lipofuscinosis

समान संसाधन

• Human recombinant palmitoyl protein thioesterase-1 (PPT1) for preclinical evaluation of enzyme replacement therapy for infantile neuronal ceroid lipofuscinosis
  द्वारा: Lu, Jui-Yun, और अन्य
  प्रकाशित: (2009)
• Didemnin binds to the protein palmitoyl thioesterase responsible for infantile neuronal ceroid lipofuscinosis.
  द्वारा: Crews, C M, और अन्य
  प्रकाशित: (1996)
• Lipid thioesters derived from acylated proteins accumulate in infantile neuronal ceroid lipofuscinosis: correction of the defect in lymphoblasts by recombinant palmitoyl-protein thioesterase.
  द्वारा: Lu, J Y, और अन्य
  प्रकाशित: (1996)
• Human palmitoyl protein thioesterase: evidence for lysosomal targeting of the enzyme and disturbed cellular routing in infantile neuronal ceroid lipofuscinosis.
  द्वारा: Hellsten, E, और अन्य
  प्रकाशित: (1996)
• Intravenous high-dose enzyme replacement therapy with recombinant palmitoyl-protein thioesterase reduces visceral lysosomal storage and modestly prolongs survival in a preclinical mouse model of infantile neuronal ceroid lipofuscinosis
  द्वारा: Hu, Jie, और अन्य
  प्रकाशित: (2012)