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Haem arginate in acute hereditary coproporphyria.

An 11 year old boy presented with severe acute hereditary coproporphyria. Despite supportive measures his condition deteriorated after admission. Haem arginate, started two days after presentation, produced appreciable inhibition of porphyrin precursor overproduction and clinical improvement.

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Detalhes bibliográficos
Main Authors: Manning, D J, Gray, T A
Formato: Artigo
Idioma:Inglês
Publicado em: 1991
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1793153/
https://ncbi.nlm.nih.gov/pubmed/2053800
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