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Clinical aspects of X-linked hypohidrotic ectodermal dysplasia.

Boys with X-linked hypohidrotic ectodermal dysplasia and their families were studied. Many suffered severe illness in early childhood and nearly 30% died; many had feeding problems, severe fever, atopic disease, and recurrent respiratory infections. Some infants failed to thrive. We found no consist...

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Autores principales: Clarke, A, Phillips, D I, Brown, R, Harper, P S
Formato: Artigo
Lenguaje:Inglês
Publicado: 1987
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC1778691/
https://ncbi.nlm.nih.gov/pubmed/2445301
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