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Fas and Fas ligand expression in cystic fibrosis airway epithelium

BACKGROUND—Cystic fibrosis (CF) is a genetic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene and defective expression of CFTR protein in epithelial cells. The main cause of mortality in CF is linked to chronic inflammatory and infectious airway proc...

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Autors principals: Durieu, I., Amsellem, C., Paulin, C., Chambe, M., Bienvenu, J., Bellon, G., Pacheco, Y
Format: Artigo
Idioma:Inglês
Publicat: BMJ Group 1999
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1763765/
https://ncbi.nlm.nih.gov/pubmed/10567629
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