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Adult familial cryptogenic fibrosing alveolitis in the United Kingdom

BACKGROUND—Familial cases of cryptogenic fibrosing alveolitis (CFA) have previously been reported; however, the prevalence and genetic background of this disorder are not known. The clinical and epidemiological findings of 25 families identified within the UK are reported.
METHODS—Adult pulmonary ph...

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Autori principali: Marshall, R., Puddicombe, A., Cookson, W., Laurent, G.
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Group 2000
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1745672/
https://ncbi.nlm.nih.gov/pubmed/10639533
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/thorax.55.2.143
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