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Increased mortality in cartilage-hair hypoplasia

BACKGROUND—Cartilage-hair hypoplasia (CHH) is an autosomal recessive chondrodysplasia with severe growth failure and impaired immunity. Impaired immunity may result in increased mortality.
AIMS—To follow a cohort of 120 CHH patients for mortality from 1971 to 1995.
METHODS—The overall and cause spec...

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Detalhes bibliográficos
Main Authors: Makitie, O, Pukkala, E, Kaitila, I
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Group 2001
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1718604/
https://ncbi.nlm.nih.gov/pubmed/11124791
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/adc.84.1.65
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