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D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxyacyl-CoA dehydrogenase bifunctional protein deficiency: a newly identified peroxisomal disorder.

Peroxisomal beta-oxidation proceeds from enoyl-CoA through D-3-hydroxyacyl-CoA to 3-ketoacyl-CoA by the D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxy-acyl-CoA dehydrogenase bifunctional protein (d-bifunctional protein), and the oxidation of bile-acid precursors also has been suggested as being catalyz...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Suzuki, Y, Jiang, L L, Souri, M, Miyazawa, S, Fukuda, S, Zhang, Z, Une, M, Shimozawa, N, Kondo, N, Orii, T, Hashimoto, T
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 1997
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC1716023/
https://ncbi.nlm.nih.gov/pubmed/9345094
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