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Low levels of beta hexosaminidase A in healthy individuals with apparent deficiency of this enzyme.

Appreciable beta hexosaminidase A (hex A) activity has been detected in cultured skin fibroblasts and melanoma tissue from healthy individuals previously reported as having deficiency of hex A activity indistinguishable from that of patients with Tay-Sachs disease (TSD). Identification and quantitat...

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Detaylı Bibliyografya
Asıl Yazarlar: Navon, R, Geiger, B, Yoseph, Y B, Rattazzi, M C
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 1976
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC1685065/
https://ncbi.nlm.nih.gov/pubmed/941901
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