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Gene transfer establishes primacy of striated vs. smooth muscle sarcoglycan complex in limb-girdle muscular dystrophy

Limb-girdle muscular dystrophy types 2E and F are characterized by skeletal muscle weakness and often cardiomyopathy and are due to mutations in the genes encoding β- and δ-sarcoglycan. We previously demonstrated that loss of sarcoglycans in smooth muscle leads to constrictions of the microvasculatu...

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Autors principals: Durbeej, Madeleine, Sawatzki, Shanna M., Barresi, Rita, Schmainda, Kathleen M., Allamand, Valérie, Michele, Daniel E., Campbell, Kevin P.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2003
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC166412/
https://ncbi.nlm.nih.gov/pubmed/12851463
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1537554100
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