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Lymphoedema in Hereditary Recurrent Cholestasis from Birth

An inherited disorder characterized by a combination of lymphoedema and intrahepatic cholestasis is described in a Norwegian kindred. The jaundice is evident soon after birth, and recurrent episodes occur throughout life. The oedema starts at about school age and subsequently progresses; it is due t...

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Autores principales: Aagenaes, Øystein, Sigstad, Helge, Bjørn-Hansen, Ragnar
Formato: Artigo
Lenguaje:Inglês
Publicado: 1970
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC1647491/
https://ncbi.nlm.nih.gov/pubmed/5477684
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