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Familial opsonization defect associated with fatal infantile dermatitis, infections, and histiocytosis.

Members of four generations of a family had a defect of serum opsonization for yeast phagocytosis consistent with dominant inheritance. 2 were healthy, one had chronic osteomyelitis, and the fourth developed a fatal illness in infancy characterized by exfoliative dermatitis, diarrhoea, multiple bact...

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Autors principals: Scott, H, Moynahan, E J, Risdon, R A, Harvey, B A, Soothill, J F
Format: Artigo
Idioma:Inglês
Publicat: 1975
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1544448/
https://ncbi.nlm.nih.gov/pubmed/1096830
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