Caricamento...

Somatic mosaicism: a common cause of classic disease in tumor-prone syndromes? Lessons from type 2 neurofibromatosis.

Blood samples from 125 families with classic type 2 neurofibromatosis with bilateral vestibular schwannomas were analyzed for mutations in the NF2 gene. Causative mutations were identified in 52 families. In five families, the first affected individual in the family (the index case) was a mosaic for...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Evans, D G, Wallace, A J, Wu, C L, Trueman, L, Ramsden, R T, Strachan, T
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1998
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1377392/
https://ncbi.nlm.nih.gov/pubmed/9718334
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !