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Galactocerebrosidase-deficient oligodendrocytes maintain stable central myelin by exogenous replacement of the missing enzyme in mice

Globoid cell leukodystrophy (GLD) is a lysosomal storage disease caused by genetic deficiency of galactocerebrosidase (GALC) activity. Failure in catalyzing the degradation of its major substrate, galactocerebroside, in oligodendrocytes (OLs) and Schwann cells leads to death of these myelinating cel...

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Autors principals: Kondo, Yoichi, Wenger, David A., Gallo, Vittorio, Duncan, Ian D.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1317926/
https://ncbi.nlm.nih.gov/pubmed/16352725
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0506473102
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