Decreased Elastin Deposition and High Proliferation of Fibroblasts from Costello Syndrome Are Related to Functional Deficiency in the 67-kD Elastin-Binding Protein

Схожие документы

• The 67-kD elastin/laminin-binding protein is related to an enzymatically inactive, alternatively spliced form of beta-galactosidase.
  по: Hinek, A, et al.
  Опубликовано: (1993)
• Impaired Elastic-Fiber Assembly by Fibroblasts from Patients with Either Morquio B Disease or Infantile GM1-Gangliosidosis Is Linked to Deficiency in the 67-kD Spliced Variant of β-Galactosidase
  по: Hinek, Aleksander, et al.
  Опубликовано: (2000)
• Retrovirally Mediated Overexpression of Versican V3 Reverses Impaired Elastogenesis and Heightened Proliferation Exhibited by Fibroblasts from Costello Syndrome and Hurler Disease Patients
  по: Hinek, Aleksander, et al.
  Опубликовано: (2004)
• Impaired elastin fiber assembly related to reduced 67-kD elastin-binding protein in fetal lamb ductus arteriosus and in cultured aortic smooth muscle cells treated with chondroitin sulfate.
  по: Hinek, A, et al.
  Опубликовано: (1991)
• 67-kD elastin-binding protein is a protective "companion" of extracellular insoluble elastin and intracellular tropoelastin
  Опубликовано: (1994)