Caricamento...

Turnover of beta-galactosidase in fibroblasts from patients with genetically different types of beta-galactosidase deficiency.

The turnover of lysosomal beta-galactosidase was studied in fibroblast cultures from patients with Gm1-gangliosidosis and combined beta-galactosidase and neuraminidase deficiency, which had 5-10% residual beta-galactosidase activity. beta-Galactosidase was specifically inactivated with the suicide s...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Van Diggelen, O P, Schram, A W, Sinnott, M L, Smith, P J, Robinson, D, Galjaard, H
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1981
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1163512/
https://ncbi.nlm.nih.gov/pubmed/6800355
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !