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Cystine storage in cultured myotubes from patients with nephropathic cystinosis.

Sorted muscle cells, cultured from a patient with nephropathic cystinosis, stored 100 times normal amounts of cystine. Subcellular fractionation and density-gradient centrifugation confirmed that the cystine was located in a lysosomal compartment. 2. Myoblasts from cystinotic patients in culture und...

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Bibliographic Details
Main Authors: Harper, G S, Bernardini, I, Hurko, O, Zuurveld, J, Gahl, W A
Format: Artigo
Language:Inglês
Published: 1987
Subjects:
Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC1147933/
https://ncbi.nlm.nih.gov/pubmed/3663103
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