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Collagen defects in lethal perinatal osteogenesis imperfecta.

Quantitative and qualitative abnormalities of collagen were observed in tissues and fibroblast cultures from 17 consecutive cases of lethal perinatal osteogenesis imperfecta (OI). The content of type I collagen was reduced in OI dermis and bone and the content of type III collagen was also reduced i...

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Dettagli Bibliografici
Autori principali: Bateman, J F, Chan, D, Mascara, T, Rogers, J G, Cole, W G
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1986
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1147476/
https://ncbi.nlm.nih.gov/pubmed/3827862
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