Llwytho...

Alkaptonuric Ochronosis with Aortic Valve and Joint Replacements and Femoral Fracture: A Case Report and Literature Review

Alkaptonuria is a rare autosomal recessive disorder of metabolism caused by deficiency of homogentisic acid oxidase and resulting in accumulation of homogentisic acid in collagenous structures. It is characterized by homogentisic aciduria, bluish-black discoloration of connective tissues (ochronosis...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Fisher, Alexander A., Davis, Michael W.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Marshfield Clinic Research Foundation 2004
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC1069096/
https://ncbi.nlm.nih.gov/pubmed/15931360
Tagiau: Ychwanegu Tag
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